Case 96: When it Runs in the Family

FPF is not uncommon with almost 1/6th of first-degree relatives of sporadic and familial PF showing ILA/ILD

Bhavin Jankharia

Table of Contents

Index and Table of Contents
Technical and Practice Issues * Case 11: 62-years old misdiagnosed to have interstitial lung disease - mid-inspiratory and expiratory scans * Snippet 03: Radiation risk and CT chest * Case 23: 60-years old - 40-pack years smoker - right upper lobe nodule - resolved using “mean” reconstructions…

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Lecture: NSIP and OP
This 16-mins lecture discusses NSIP and OP

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A 52-years old man presented with a probable UIP pattern in 2018.

At this age, this is indistinguisable from a fibrotic NSIP pattern. He was a non-smoker and had no etiology including connective tissue disease (CTD).

He progressed and had a successful lung transplant.

8 years later, his elder brother presented with mild breathlessness and a CT scan shows a typical UIP pattern.

The video runs through both cases and then discusses the findings in a third brother with a detailed discussion of the current concepts related to familial pulmonary fibrosis (FPF).

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Snippet 04: Fibrotic NSIP vs Probable UIP

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