Case 96: When it Runs in the Family

FPF is not uncommon with almost 1/6th of first-degree relatives of sporadic and familial PF showing ILA/ILD

Bhavin Jankharia

Table of Contents

Index and Table of Contents
Technical and Practice Issues * Case 11: 62-years old misdiagnosed to have interstitial lung disease - mid-inspiratory and expiratory scans * Snippet 03: Radiation risk and CT chest * Case 23: 60-years old - 40-pack years smoker - right upper lobe nodule - resolved using “mean” reconstructions…

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Lecture: NSIP and OP
This 16-mins lecture discusses NSIP and OP

Current Post

A 52-years old man presented with a probable UIP pattern in 2018.

At this age, this is indistinguisable from a fibrotic NSIP pattern. He was a non-smoker and had no etiology including connective tissue disease (CTD).

He progressed and had a successful lung transplant.

8 years later, his elder brother presented with mild breathlessness and a CT scan shows a typical UIP pattern.

The video runs through both cases and then discusses the findings in a third brother with a detailed discussion of the current concepts related to familial pulmonary fibrosis (FPF).


For those seeing this on email.
Please note that the video only plays within this browser page and not outside of this browser page. If the video does not autoplay in your email, then you will need to open this page in your browser, by clicking "View Online", in the 2nd line below the title of the post and next to my name.

My New Book

The Book - Atmasvasth - A Guide to Ageing Healthfully
A 15-point guide to living long, healthy

Other Sites and Cases

Case 141: Thymic Mass Biopsy, Seeding Issues, etc
Suspected thymic mass biopsies are safe and simple and seeding is not an issue.
Physical Activity Update - II (What, When, How Much)
Updated data on the impact of strength training and the step count needed and the “weekend warrior” phenomenon
Case 43: Diffuse and Focal
14-years old with pain in both hips, right knee and generalized weakness
IPFILDFamilial Pulmonary Fibrosis

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Featured Posts

Case 98: Acute Increased Dyspnea in Idiopathic Pulmonary Fibrosis - First Considerations

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Case 96: When it Runs in the Family

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REF-Cafe Roentgen Thoracic Thursday Lecture - XII - 26th Oct 2023: Mediastinum

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REF-Cafe Roentgen Thoracic Thursday Lecture - XI - 19th Oct 2023: Non-Resolving Opacity

Case 91: Bubble Lucencies, Central Lucencies, Bubbly Consolidation

Case 90: The Probable UIP Conundrum - Time Matters

REF-Cafe Roentgen Thoracic Thursday Lecture - X - 21st Sep 2023: Solitary Pulmonary Nodule - III - Subsolid Nodule

Case 89: Diaphragmatic Dysfunction – Eventration, Paralysis…Does it Matter

REF-Cafe Roentgen Thoracic Thursday Lecture - IX - 14th Sep 2023: Solitary Pulmonary Nodule - PFN, Juxtrapleural Nodule, Nodules in Smokers and Lung-RADs

REF-Cafe Roentgen Thoracic Thursday Lecture - VIII - 07th Sep 2023: Solitary Pulmonary Nodule > 8 mm

Snippet 17: How to Diagnose Subtle Progression of Interstitial Lung Disease at the Secondary Pulmonary Lobule Level

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REF-Cafe Roentgen Thoracic Thursday Lecture - VII - 10th Aug 2023: Diffuse Cystic Lung Disease

REF-Cafe Roentgen Thoracic Thursday Lecture - VI - 03rd Aug 2023: Smoking Related Lung Diseases

Snippet 16: Inflammatory vs Fibrotic ILD

REF-Cafe Roentgen Thoracic Thursday Lecture - V - 20th July 2023: All About the Centrilobular Nodule

REF-Cafe Roentgen Thoracic Thursday Lecture - IV - 13th July 2023: Non-ILD Diffuse Lung Diseases

Case 87: Thymic Cyst or Cystic Thymoma

REF-Cafe Roentgen Thoracic Thursday Lecture - III - 29th June 2023: Non-Fibrosing ILDs

REF-Cafe Roentgen Thoracic Thursday Lecture - II - 22nd June 2023: Fibrosing ILDs - contd & Introduction to Non-Fibrosing ILDs

REF-Cafe Roentgen Thoracic Thursday Lecture - I: Fibrosing ILDs - 2023 06 15

Approach to Small Diffuse Lung Nodules - Lecture

Snippet 09: Variant Fibrosis

Snippet 08: Mosaic Attenuation

Snippet 04: Fibrotic NSIP vs Probable UIP

Snippet 02: Centrilobular / Bronchocentric Nodules

Snippet 01: Differentiating Traction Bronchiectasis from Honeycombing