Case 96: When it Runs in the Family

FPF is not uncommon with almost 1/6th of first-degree relatives of sporadic and familial PF showing ILA/ILD

Bhavin Jankharia

Table of Contents

Index and Table of Contents
Technical and Practice Issues * Case 11: 62-years old misdiagnosed to have interstitial lung disease - mid-inspiratory and expiratory scans * Snippet 03: Radiation risk and CT chest * Case 23: 60-years old - 40-pack years smoker - right upper lobe nodule - resolved using “mean” reconstructions…

Previous Post

Lecture: NSIP and OP
This 16-mins lecture discusses NSIP and OP

Current Post

A 52-years old man presented with a probable UIP pattern in 2018.

At this age, this is indistinguisable from a fibrotic NSIP pattern. He was a non-smoker and had no etiology including connective tissue disease (CTD).

He progressed and had a successful lung transplant.

8 years later, his elder brother presented with mild breathlessness and a CT scan shows a typical UIP pattern.

The video runs through both cases and then discusses the findings in a third brother with a detailed discussion of the current concepts related to familial pulmonary fibrosis (FPF).


For those seeing this on email.
Please note that the video only plays within this browser page and not outside of this browser page. If the video does not autoplay in your email, then you will need to open this page in your browser, by clicking "View Online", in the 2nd line below the title of the post and next to my name.

My New Book

The Book - Atmasvasth - A Guide to Ageing Healthfully
A 15-point guide to living long, healthy

Other Sites and Cases

Case 141: Thymic Mass Biopsy, Seeding Issues, etc
Suspected thymic mass biopsies are safe and simple and seeding is not an issue.
Physical Activity Update - II (What, When, How Much)
Updated data on the impact of strength training and the step count needed and the “weekend warrior” phenomenon
Case 43: Diffuse and Focal
14-years old with pain in both hips, right knee and generalized weakness
IPFILDFamilial Pulmonary Fibrosis

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